Late Onset Ataxia: A Case Report

Year : 2024 | Volume :14 | Issue : 01 | Page : 16-20
By

    Praveen Kumar Yadav

  1. Shweta Moreshwar Bawankar

  1. Senior Consultant Neurologist, Director of Aarogyam, Neuroclinic & Associate Professor, SRIMS (Shri Ramkrishna Institute of Medical Sciences, West Bengal, India
  2. Diplomate of National Board Medicine Trainee, DSP (Durgapur Steel Plant) Hospital, West Bengal, India

Abstract

57-year-old man with no prior history of any illness presented with subacute onset of gradually progressive gait ataxia, upper limb incoordination and speech issues. There was history suggestive of orthostatic hypotension and erectile dysfunction. On examination, there was normal cognition with gaze evoked nystagmus, scanning speech and limb incoordination in the form of past pointing, dysdiadochokinesia, and tandem walking abnormality suggestive of pan cerebellar involvement. The patient was evaluated with routine investigations which were normal including liver, thyroid, and renal function tests. MRI Brain showed Hot cross bun sign and cerebellar atrophy. Secondly, secondary causes of subacute ataxia like ANA Profile, Autoimmune and paraneoplastic antibody panel was negative which included anti GAD Antibodies. CT Chest and CT Abdomen as a part of paraneoplastic work up was negative. CSF Study was normal. In view of classical history, examination findings and MRI Brain features with negative autoimmune and paraneoplastic workup a diagnosis of Multisystem Atrophy-C was made, and patient was managed symptomatically and is under follow up

Keywords: MSA Parkinsons plus ataxia dysautonomia, Gait ataxia, Speech issues, Scanning speech, Hot cross bun sign, MRI Brain, CT Chest and CT Abdomen.

[This article belongs to Research & Reviews: A Journal of Neuroscience(rrjons)]

How to cite this article: Praveen Kumar Yadav, Shweta Moreshwar Bawankar.Late Onset Ataxia: A Case Report.Research & Reviews: A Journal of Neuroscience.2024; 14(01):16-20.
How to cite this URL: Praveen Kumar Yadav, Shweta Moreshwar Bawankar , Late Onset Ataxia: A Case Report rrjons 2024 {cited 2024 Apr 19};14:16-20. Available from: https://journals.stmjournals.com/rrjons/article=2024/view=143698


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Regular Issue Subscription Case Study
Volume 14
Issue 01
Received December 26, 2023
Accepted January 23, 2024
Published April 19, 2024
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